Monday, May 25, 2009

164 - Marfan's syndrome mcqs with answers part 1

1q: the triad of features characteristic of marfan’s syndrome are all except ?


a. skeletal changes that include long, thin extremities, frequently associated with loose joints
b. reduced vision as the result of dislocation of the lenses (ectopia lentis)
c. aortic root dilation and aortic aneurysms
d. hypertrophic cardiomyopathy






2q: what is the mutation seen in type 1 marfan’s syndrome ?


a. fibrillin-1 ( FBN1 ) gene
b. transforming growth factor beta receptor 2 ( TGFBR2 ) gene
c. nephrin gene
d. tubulin gene






3q: what is the mutation most commonly associated with type 2 marfan’s syndrome ?


a. fibrillin-1 ( FBN1 )gene
b. transforming growth factor beta receptor 2 ( TGFBR2 ) gene
c. nephrin gene
d. tubulin gene






4q: type 2 marfan’s syndrome patients are similar to type 1 marfan’s syndrome patients in all except ?


a. skeletal changes
b. ocular changes
c. aortic aneursyms
d. heart valve diseases






5q: mutations in both TGFB1 and TGFB2 genes are found in which syndrome ?


a. Kelly seeg miller syndrome
b. Loeys-dietz aneurysm syndrome ( LDAS )
c. Capgras syndrome
d. Lafora’s syndrome


No comments:

Subscribe Now: Feed

You are visitor number

Visitors currently online